Здравоохранение Кыргызстана
Zdravoohraneniye Kyrgyzstana
ISSN 1694-8068 (Print)
ISSN 1694-805X (Online)

POEMS синдром, сложности диагностики

POEMS синдром, сложности диагностики
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Аннотация

POEMS syndrome редкое мультисистемное заболевание, вызванное циркулирующими в крови иммуноглобулинами вследствие плазмоцитарной дискразии. POES – это собирательная аббревиатура: P –polyneuropathy (по- линейропатия), O- organomegaly (органомегалия), E –Endocrinopathy (эндокринопатия), M- M-protein (М-протеинемия), S – skin change (кожные изменения). Основными клиническими признаками этого синдрома является прогрессирующая полинейропатия с преобладанием двигательных нарушений. Заболевание потенциально смертельно, и качество жизни пациента ухудшается из-за прогрессирующей невропатии, массивного периферического отека, плеврального выпота и асцита. Серьезные осложнения, такие как полиорганная недостаточность, рестриктивная болезнь легких и легочная гипертензия, приводят к неблагоприятному прогнозу.

Об авторах

Нурбекова Улболсун Ажибековна, врач-невролог Центра лучевой диагностики ЮРФА,Бишкек, Кыргызская
Республика;
Муканбетова Гулзат Догдурбаевна, ассистент кафедры неврологии и клинической генетики КГМА им.акад.Ахунбаева И.К., Бишкек, Кыргызская Республика.

Nurbekova Ulbolsun Azhibekovna, neurologist of the Center for Radiation Diagnostics of YURFA, Bishkek, Kyrgyz
Republic;
Mukanbetova Gulzat Dogdurbaevna, assistant of the Department of Neurology and Clinical Genetics of KGMA
named after Akad. Akhunbaeva I.K., Bishkek, Kyrgyz Republic.

Нурбекова Улболсун Ажибековна, нурология диагностикасы борборунун неврологу, ЮРФА, Бишкек, Кыргыз Республикасы;

Муканбетова Гүлзат Догдурбаевна, И.К. Ахунбаев атындагы КММАнын неврология жана клиникалык генетика кафедрасынын ассистенти, Бишкек, Кыргыз Республикасы.

Список литературы

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

 

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

Для цитирования

Нурбекова У.А., Муканбетова Г.Д. POEMS синдром, сложности диагностики. Здравоохранение Кыргызстана 2021, № 3, с. 96-103;

https://doi.org/10.51350/zdravkg2021931396

For citation

Nurbekova U.A. , Mukanbetova G.D. POEMS syndrome, difficulty diagnosis.Health care of Kyrgyzstan 2021, no 3, pp. 96-103;

https://doi.org/10.51350/zdravkg2021931396

Цитата үчүн

Нурбекова У.А., Муканбетова Г.Д. POEMS синдром, диагноз коюдагы кыйынчылыктар. Кыргызстандын Cаламаттык Cактоо 2021, № 3, б. 96-103;  


https://doi.org/10.51350/zdravkg2021931396

Авторы Нурбекова У.А., Муканбетова Г.Д.
Ссылка doi.org https://doi.org/10.51350/zdravkg2021931396
Страницы 96-103
Русский
Об авторах

Нурбекова Улболсун Ажибековна, врач-невролог Центра лучевой диагностики ЮРФА,Бишкек, Кыргызская
Республика;
Муканбетова Гулзат Догдурбаевна, ассистент кафедры неврологии и клинической генетики КГМА им.акад.Ахунбаева И.К., Бишкек, Кыргызская Республика.

Полный текст

PDF (RUS)

Список литературы

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

 

Для цитирования

Нурбекова У.А., Муканбетова Г.Д. POEMS синдром, сложности диагностики. Здравоохранение Кыргызстана 2021, № 3, с. 96-103;

https://doi.org/10.51350/zdravkg2021931396

Английский
About authors

Nurbekova Ulbolsun Azhibekovna, neurologist of the Center for Radiation Diagnostics of YURFA, Bishkek, Kyrgyz
Republic;
Mukanbetova Gulzat Dogdurbaevna, assistant of the Department of Neurology and Clinical Genetics of KGMA
named after Akad. Akhunbaeva I.K., Bishkek, Kyrgyz Republic.

Full text

PDF (RUS)

References

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

For citation

Nurbekova U.A. , Mukanbetova G.D. POEMS syndrome, difficulty diagnosis.Health care of Kyrgyzstan 2021, no 3, pp. 96-103;

https://doi.org/10.51350/zdravkg2021931396

Кыргызский
Авторлор жөнүндө

Нурбекова Улболсун Ажибековна, нурология диагностикасы борборунун неврологу, ЮРФА, Бишкек, Кыргыз Республикасы;

Муканбетова Гүлзат Догдурбаевна, И.К. Ахунбаев атындагы КММАнын неврология жана клиникалык генетика кафедрасынын ассистенти, Бишкек, Кыргыз Республикасы.

Толук текст

PDF (RUS)

Шилтемелер

1. Nakanishi T., Sobue I., Toyokura Y. et al. The Crow-Fukase syndrome: a study of 102 cases in Japan. Neurology 1984; 34: 712—720.
2. Bardwick P. A., Zvaif ler N. J., Gill G. N. Plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes: the POEMS syndrome. Report on two cases and a review of the literature. Medicine (Baltimore) 1980; 4:311–22.
3. Rison R. A., Beydoun S. R. Paraproteinemic polyneuropathy: apractical review // BMC Neurology. — 2016. — Vol. 16. — №13. — P. 1 — 14.
4.Takatsuki K., Yodoi J., Wikasaka K. et al. Plasma cell dyscrasia with polyneuritis and an endocrine anomaly: endocrinological study of a new syndrome. Nippon Rinsho 1974;50: 2444—2456.
5. Klodzinsky A.A., Ryzhko V.V., Sorkina O.M. POEMS-syndrome(describtion of observation and literature review) // Clinical hematology oncology. 2008 Vol. 1, No. 2 P. 145-155
6. A.Nozza. POEMS syndrome. Mediterranean Journal pf Hematology and Infectious Diseases

7. Ginxburg M.A. Demyelinating pilyneuropaties assotiated with paraproteiemia (clinical, electrophysiological and immunological research): dis…can.honey. Sciences: 14.01.11. – «Scientific Center of Neurology», Moscow, 2015-152s.
8. Lavenstain B., Dalakas M., Engel W.K. et al. Polyneuropathy in non-secretory osteosclerotic multiple myeloma with immunoglobulin deposition in peripheral nerve tissue. Neurology 1979; 29: 611.
9.Dispenzieri A. POEMS syndrome: update on diagnosis, riskstratification,and management. Am J Hematology 2012; 87:
805—814.
10. R.Brown., L.Ginsberg Journal of Neurology 2019; 266 (1) 268-277
11. Barlamov P.N., Golubeva M.E., Vasilieva E.R. A case of late diagnosis of POEMS syndrome // Clinical 2011, No. 4, T.5
12. Dispenzieri A., Kyle R. Ava 2014, no.4, pp. 4-10., Lacy M. Q. et al. POEMS syndrome: definitions and long-term outcome.Blood 2003; 101: 2496–506. Piradov MA, Suponeva NA, Ginzberg MA, POEMS-syndrome: a literature review and description of clinical observations //Journal of Neurology and Psychiatry. S.S. Korsako

Цитата үчүн

Нурбекова У.А., Муканбетова Г.Д. POEMS синдром, диагноз коюдагы кыйынчылыктар. Кыргызстандын Cаламаттык Cактоо 2021, № 3, б. 96-103;  


https://doi.org/10.51350/zdravkg2021931396

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ISSN 1694-8068 (Print)
ISSN 1694-805X (Online)